Glycogen Debranching Enzyme (AGL)
GDE; Amylo-1,6-Glucosidase; 4-Alpha-Glucanotransferase; Glycogen debrancher; 4-alpha-glucanotransferase; Oligo-1,4-1,4-glucantransferase; Dextrin 6-alpha-D-glucosidase
Debranching enzymes are responsible for transferring three glucose subunits of glycogen from one parallel chain to another. Afterwards, the donator branch will contain only one glucose residue with alpha-1,6 linkage. This remaining residue is in turn cut by alpha-1,6 glucosidase. This two step process is the general process by which the debranching enzymes "straighten out" glycogen into an unbranched glucose polymer.This enzyme has two independent catalytic activities which occur at different sites on the protein: a 4-alpha-glucotransferase activity and a amylo-1,6-glucosidase activity. Mutations in this gene are associated with glycogen storage disease although a wide range of enzymatic and clinical variability occurs which may be due to tissue-specific alternative splicing.
Organism species: Homo sapiens (Human)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | RPD189Hu01 | Recombinant Glycogen Debranching Enzyme (AGL) | Positive Control; Immunogen; SDS-PAGE; WB. |
Antibodies | PAD189Hu01 | Polyclonal Antibody to Glycogen Debranching Enzyme (AGL) | WB; IHC; ICC; IP. |
Assay Kits | SED189Hu | ELISA Kit for Glycogen Debranching Enzyme (AGL) | Enzyme-linked immunosorbent assay for Antigen Detection. |
Organism species: Mus musculus (Mouse)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | RPD189Mu01 | Recombinant Glycogen Debranching Enzyme (AGL) | Positive Control; Immunogen; SDS-PAGE; WB. |
Antibodies | PAD189Mu01 | Polyclonal Antibody to Glycogen Debranching Enzyme (AGL) | WB; IHC; ICC; IP. |
Assay Kits | n/a | CLIA Kit for Glycogen Debranching Enzyme (AGL) | CLIA Kit Customized Service Offer |
n/a | ELISA Kit for Glycogen Debranching Enzyme (AGL) | ELISA Kit Customized Service Offer |
Organism species: Rattus norvegicus (Rat)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | n/a | Recombinant Glycogen Debranching Enzyme (AGL) | Recombinant Protein Customized Service Offer |
Antibodies | n/a | Monoclonal Antibody to Glycogen Debranching Enzyme (AGL) | Monoclonal Antibody Customized Service Offer |
n/a | Polyclonal Antibody to Glycogen Debranching Enzyme (AGL) | Polyclonal Antibody Customized Service Offer | |
Assay Kits | n/a | CLIA Kit for Glycogen Debranching Enzyme (AGL) | CLIA Kit Customized Service Offer |
n/a | ELISA Kit for Glycogen Debranching Enzyme (AGL) | ELISA Kit Customized Service Offer |