Atrophin 1 (ATN1)

B37; DRPLA; NOD; Dentatorubral Pallidoluysian Atrophy

ATN1 is a protein found in nervous tissue. It is associated with a form of trinucleotide repeat disorder known as "dentatorubral-pallidoluysian atrophy" or "dentatorubropallidoluysian atrophy".
Dentatorubral pallidoluysian atrophy is a rare neurodegenerative disorder characterized by cerebellar ataxia, myoclonic epilepsy, choreoathetosis, and dementia. The disorder is related to the expansion of a trinucleotide repeat within this gene. The encoded protein includes a serine repeat and a region of alternating acidic and basic amino acids, as well as the variable glutamine repeat. Alternative splicing results in two transcripts variants that encode the same protein.

Organism species: Homo sapiens (Human)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPC225Hu01 Recombinant Atrophin 1 (ATN1) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies PAC225Hu01 Polyclonal Antibody to Atrophin 1 (ATN1) WB; IHC; ICC; IP.
MAC225Hu21 Monoclonal Antibody to Atrophin 1 (ATN1) WB; IHC; ICC; IP.
Assay Kits SEC225Hu ELISA Kit for Atrophin 1 (ATN1) Enzyme-linked immunosorbent assay for Antigen Detection.

Organism species: Mus musculus (Mouse)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Atrophin 1 (ATN1) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Atrophin 1 (ATN1) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Atrophin 1 (ATN1) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Atrophin 1 (ATN1) CLIA Kit Customized Service Offer
n/a ELISA Kit for Atrophin 1 (ATN1) ELISA Kit Customized Service Offer

Organism species: Rattus norvegicus (Rat)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Atrophin 1 (ATN1) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Atrophin 1 (ATN1) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Atrophin 1 (ATN1) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Atrophin 1 (ATN1) CLIA Kit Customized Service Offer
n/a ELISA Kit for Atrophin 1 (ATN1) ELISA Kit Customized Service Offer