Aminolevulinate Delta Synthase 1 (ALAS1)
ALAS3; ALAS; ALASH; 5-aminolevulinic acid synthase 1; Delta-ALA synthase 1; 5-aminolevulinate synthase, nonspecific, mitochondrial
Delta-aminolevulinate synthase 1 is an aminolevulinic acid synthase. Delta-aminolevulinate synthase catalyzes the condensation of glycine with succinyl-CoA to form delta-aminolevulinic acid. This nuclear-encoded mitochondrial enzyme is the first and rate-limiting enzyme in the mammalian heme biosynthetic pathway. There are 2 tissue-specific isozymes: a housekeeping enzyme encoded by the ALAS1 gene and an erythroid tissue-specific enzyme encoded by ALAS2.
ALAS1encodes a housekeeping form of ALAS inasmuch as it is expressed in all cell types, including erythroid cells, whereas ALAS2 encodes a red cell-specific form. ALAS1 and ALAS2 have only 59% identity in amino acid sequence; there was no homology in the amino-terminal region and about 73% homology after hepatic residue 197.
Organism species: Homo sapiens (Human)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | n/a | Recombinant Aminolevulinate Delta Synthase 1 (ALAS1) | Recombinant Protein Customized Service Offer |
Antibodies | n/a | Monoclonal Antibody to Aminolevulinate Delta Synthase 1 (ALAS1) | Monoclonal Antibody Customized Service Offer |
n/a | Polyclonal Antibody to Aminolevulinate Delta Synthase 1 (ALAS1) | Polyclonal Antibody Customized Service Offer | |
Assay Kits | n/a | CLIA Kit for Aminolevulinate Delta Synthase 1 (ALAS1) | CLIA Kit Customized Service Offer |
n/a | ELISA Kit for Aminolevulinate Delta Synthase 1 (ALAS1) | ELISA Kit Customized Service Offer |
Organism species: Mus musculus (Mouse)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | n/a | Recombinant Aminolevulinate Delta Synthase 1 (ALAS1) | Recombinant Protein Customized Service Offer |
Antibodies | n/a | Monoclonal Antibody to Aminolevulinate Delta Synthase 1 (ALAS1) | Monoclonal Antibody Customized Service Offer |
n/a | Polyclonal Antibody to Aminolevulinate Delta Synthase 1 (ALAS1) | Polyclonal Antibody Customized Service Offer | |
Assay Kits | n/a | CLIA Kit for Aminolevulinate Delta Synthase 1 (ALAS1) | CLIA Kit Customized Service Offer |
n/a | ELISA Kit for Aminolevulinate Delta Synthase 1 (ALAS1) | ELISA Kit Customized Service Offer |
Organism species: Rattus norvegicus (Rat)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | RPF209Ra01 | Recombinant Aminolevulinate Delta Synthase 1 (ALAS1) | Positive Control; Immunogen; SDS-PAGE; WB. |
Antibodies | PAF209Ra01 | Polyclonal Antibody to Aminolevulinate Delta Synthase 1 (ALAS1) | WB; IHC; ICC; IP. |
MAF209Ra21 | Monoclonal Antibody to Aminolevulinate Delta Synthase 1 (ALAS1) | WB; IHC; ICC; IP. | |
Assay Kits | SEF209Ra | ELISA Kit for Aminolevulinate Delta Synthase 1 (ALAS1) | Enzyme-linked immunosorbent assay for Antigen Detection. |