Adenylosuccinate Lyase (ADSL)

AMPS; ASase; Adenylosuccinase

Adenylsuccinate lyase is involved in both de novo synthesis of purines and formation of adenosine monophosphate from inosine monophosphate. It catalyzes two reactions in AMP biosynthesis: the removal of a fumarate from succinylaminoimidazole carboxamide (SAICA) ribotide to give aminoimidazole carboxamide ribotide (AICA) and removal of fumarate from adenylosuccinate to give AMP.
Adenylosuccinase deficiency results in succinylpurinemic autism, psychomotor retardation, and , in some cases, growth retardation associated with muscle wasting and epilepsy. Two transcript variants encoding different isoforms have been found for this gene. Ubiquitously expressed. Both isoforms are produced by all tissues.

Organism species: Homo sapiens (Human)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPG452Hu01 Recombinant Adenylosuccinate Lyase (ADSL) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies n/a Monoclonal Antibody to Adenylosuccinate Lyase (ADSL) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Adenylosuccinate Lyase (ADSL) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Adenylosuccinate Lyase (ADSL) CLIA Kit Customized Service Offer
n/a ELISA Kit for Adenylosuccinate Lyase (ADSL) ELISA Kit Customized Service Offer

Organism species: Mus musculus (Mouse)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Adenylosuccinate Lyase (ADSL) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Adenylosuccinate Lyase (ADSL) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Adenylosuccinate Lyase (ADSL) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Adenylosuccinate Lyase (ADSL) CLIA Kit Customized Service Offer
n/a ELISA Kit for Adenylosuccinate Lyase (ADSL) ELISA Kit Customized Service Offer

Organism species: Rattus norvegicus (Rat)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Adenylosuccinate Lyase (ADSL) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Adenylosuccinate Lyase (ADSL) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Adenylosuccinate Lyase (ADSL) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Adenylosuccinate Lyase (ADSL) CLIA Kit Customized Service Offer
n/a ELISA Kit for Adenylosuccinate Lyase (ADSL) ELISA Kit Customized Service Offer